Relapsing polychondritis

M13_RELAPSPOLYCHONDR

relapsing polychondritis: Relapsing polychondritis (RP) is a rare, clinically heterogeneous, multisystemic inflammatory disease characterized by inflammation of the cartilage and proteoglycan rich structures leading to cartilage damage with joint, ocular and cardiovascular involvement.

Endpoint definition

FinnGen phenotype data

392423 individuals

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Apply sex-specific rule None

392423

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Check conditions None

392423

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Check pre-conditions, main-only, mode, registry filters

Hospital Discharge: ICD-10 M94.1
Cause of death: ICD-10 M94.1

2 out of 7 registries used, show all original rules.

53

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Check minimum number of events None

53

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Include endpoints None

53

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Remove individuals based on genotype QC

50

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M13_RELAPSPOLYCHONDR

Control definitions

Control exclude M13_OTHERBONE

Extra metadata

Level in the ICD hierarchy 4
First used in FinnGen datafreeze DF2
Parent code in ICD-10 M94
Name in latin Polychondritis recidiva

Summary Statistics

Key figures

All Female Male
Number of individuals 50 38 12
Unadjusted prevalence (%) 0.01 0.02 0.01
Mean age at first event (years) 50.63 49.18 55.20

Mortality

Follow-up Absolute risk HR [95% CI] p N
1998–2019 - - - -
15 years - - - -
5 years - - - -
1 year - - - -

Age distribution of first events

Year distribution of first events

Cumulative Incidence

Correlations

Index endpoint: M13_RELAPSPOLYCHONDR – Relapsing polychondritis
GWS hits:

Survival analyses between endpoints

Plot

before Relapsing polychondritis
after Relapsing polychondritis

loading spinner Loading survival analyses plot

Drugs most likely to be purchased after Relapsing polychondritis

Endpoint not on priority list, no data to show.