| Source | Code | Name | Case count | Share of cases (%) |
|---|---|---|---|---|
| OUTPAT | OUTPAT_ICD10(Q8500) | Neurofibromatosis, type 1 | 171 | |
| OUTPAT | OUTPAT_ICD10(Q8509) | Unspecified neurofibromatosis | 105 | |
| INPAT | INPAT_ICD10(Q8500) | Neurofibromatosis, type 1 | 96 | |
| OUTPAT | OUTPAT_ICD10(Q851) | Tuberous sclerosis | 60 | |
| INPAT | INPAT_ICD10(Q8509) | Unspecified neurofibromatosis | 53 | |
| OUTPAT | OUTPAT_ICD10(Q8501) | Neurofibromatosis, type 2 | 46 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q8500) | Neurofibromatosis, type 1. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 46 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q850) | Neurofibromatosis (nonmalignant). Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 37 | |
| OUTPAT | OUTPAT_ICD10(Q850) | Neurofibromatosis (nonmalignant) | 33 | |
| INPAT | INPAT_ICD10(Q851) | Tuberous sclerosis | 27 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q8509) | Unspecified neurofibromatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 24 | |
| OUTPAT | OUTPAT_ICD10(Q8582) | of Hipple-Lindau syndrome | 21 | |
| OUTPAT | OUTPAT_ICD10(Q859) | Phakomatosis, unspecified | 20 | |
| INPAT | INPAT_ICD10(Q8501) | Neurofibromatosis, type 2 | 19 | |
| INPAT | INPAT_ICD10(Q850) | Neurofibromatosis (nonmalignant) | 18 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q851) | Tuberous sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 17 | |
| INPAT | INPAT_ICD10(Q8582) | of Hipple-Lindau syndrome | 13 | |
| OUTPAT | OUTPAT_ICD10(Q8580) | Peutz-Jegher syndrome | 10 | |
| OUTPAT | OUTPAT_ICD10(Q8583) | Gardner syndrome | 9 | |
| OUTPAT | OUTPAT_ICD10(Q8588) | Other phakomatoses, not elsewhere classified | 9 | |
| INPAT | INPAT_ICD10(Q859) | Phakomatosis, unspecified | 8 | |
| OUTPAT | OUTPAT_ICD10(Q8581) | Sturge-Weber syndrome | 8 | |
| DEATH | DEATH_ICD10(Q850) | Neurofibromatosis (nonmalignant) | 6 | |
| INPAT | INPAT_ICD10(Q8581) | Sturge-Weber syndrome | 6 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q8501) | Neurofibromatosis, type 2. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 6 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(Q8582) | of Hipple-Lindau syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 6 |