| Source | Code | Name | Case count | Share of cases (%) |
|---|---|---|---|---|
| OUTPAT | OUTPAT_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 847 | |
| INPAT | INPAT_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica | 493 | |
| OUTPAT | OUTPAT_ICD10(M313) | Wegener's granulomatosis | 409 | |
| INPAT | INPAT_ICD10(M313) | Wegener's granulomatosis | 298 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M315) | Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 277 | |
| OUTPAT | OUTPAT_ICD10(M319) | Necrotizing vasculopathy, unspecified | 187 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M313) | Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 145 | |
| OUTPAT | OUTPAT_ICD10(M317) | Microscopic polyangiitis | 142 | |
| INPAT | INPAT_ICD10(M319) | Necrotizing vasculopathy, unspecified | 112 | |
| OUTPAT | OUTPAT_ICD10(M318) | Other specified necrotizing vasculopathies | 94 | |
| INPAT | INPAT_ICD10(M317) | Microscopic polyangiitis | 78 | |
| INPAT | INPAT_ICD10(M318) | Other specified necrotizing vasculopathies | 49 | |
| INPAT | INPAT_ICD9(4476A) | Arteritis, unspecified | 47 | |
| OUTPAT | OUTPAT_ICD10(M314) | Aortic arch syndrome [Takayasu] | 42 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M317) | Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 29 | |
| INPAT | INPAT_ICD10(M314) | Aortic arch syndrome [Takayasu] | 28 | |
| INPAT | INPAT_ICD8(44698) | Polyarteritis nodosa and allied conditions, Other | 27 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M319) | Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 27 | |
| DEATH | DEATH_ICD10(M313) | Wegener's granulomatosis | 22 | |
| INPAT | INPAT_ICD9(4464A) | Wegener's granulomatosis | 18 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M314) | Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 13 | |
| PRIM_OUT | PRIM_OUT_NOT_USED_ICD10(M318) | Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! | 11 | |
| INPAT | INPAT_ICD9(4467A) | Takayasu's disease | 7 | |
| DEATH | DEATH_ICD10(M317) | Microscopic polyangiitis | 5 |