Source Code Name Case count Share of cases (%)
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M353) Polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 3229
OUTPAT OUTPAT_ICD10(M353) Polymyalgia rheumatica 2996
OUTPAT OUTPAT_ICD10(M350) Sicca syndrome [Sjögren] 2362
INPAT INPAT_ICD10(M353) Polymyalgia rheumatica 1610
OUTPAT OUTPAT_ICD10(M357) Hypermobility syndrome 1359
OUTPAT OUTPAT_ICD10(M359) Systemic involvement of connective tissue, unspecified 1347
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M350) Sicca syndrome [Sjögren]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 1107
OUTPAT OUTPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 847
OUTPAT OUTPAT_ICD10(M329) Systemic lupus erythematosus, unspecified 813
INPAT INPAT_ICD10(M350) Sicca syndrome [Sjögren] 788
INPAT INPAT_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica 493
OUTPAT OUTPAT_ICD10(M351) Other overlap syndromes 489
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M357) Hypermobility syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 429
INPAT INPAT_ICD10(M329) Systemic lupus erythematosus, unspecified 409
OUTPAT OUTPAT_ICD10(M313) Wegener's granulomatosis 409
OUTPAT OUTPAT_ICD10(M341) CR(E)ST syndrome 375
INPAT INPAT_ICD10(M359) Systemic involvement of connective tissue, unspecified 363
INPAT INPAT_ICD10(M357) Hypermobility syndrome 299
INPAT INPAT_ICD10(M313) Wegener's granulomatosis 298
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M329) Systemic lupus erythematosus, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 287
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M315) Giant cell arteritis with polymyalgia rheumatica. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 277
OUTPAT OUTPAT_ICD10(M349) Systemic sclerosis, unspecified 261
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M359) Systemic involvement of connective tissue, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 236
OUTPAT OUTPAT_ICD10(M321) Systemic lupus erythematosus with organ or system involvement 227
OUTPAT OUTPAT_ICD10(M328) Other forms of systemic lupus erythematosus 227
OUTPAT OUTPAT_ICD10(M332) Polymyositis 196
OUTPAT OUTPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 187
INPAT INPAT_ICD10(M351) Other overlap syndromes 177
OUTPAT OUTPAT_ICD10(M316) Other giant cell arteritis 175
OUTPAT OUTPAT_ICD10(M320) Drug-induced systemic lupus erythematosus 169
INPAT INPAT_ICD9(7100A) Systemic lupus erythematosus 159
INPAT INPAT_ICD10(M321) Systemic lupus erythematosus with organ or system involvement 154
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M341) CR(E)ST syndrome. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 146
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M313) Wegener's granulomatosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 145
OUTPAT OUTPAT_ICD10(M317) Microscopic polyangiitis 142
OUTPAT OUTPAT_ICD10(M358) Other specified systemic involvement of connective tissue 142
OUTPAT OUTPAT_ICD10(M339) Dermatopolymyositis, unspecified 134
OUTPAT OUTPAT_ICD10(M355) Multifocal fibrosclerosis 132
OUTPAT OUTPAT_ICD10(M311) Thrombotic microangiopathy 127
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M351) Other overlap syndromes. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 126
OUTPAT OUTPAT_ICD10(M331) Other dermatomyositis 124
OUTPAT OUTPAT_ICD10(M300) Polyarteritis nodosa 122
INPAT INPAT_ICD10(M341) CR(E)ST syndrome 118
INPAT INPAT_ICD10(M332) Polymyositis 113
INPAT INPAT_ICD10(M319) Necrotizing vasculopathy, unspecified 112
OUTPAT OUTPAT_ICD10(M340) Progressive systemic sclerosis 109
OUTPAT OUTPAT_ICD10(M310) Hypersensitivity angiitis 97
INPAT INPAT_ICD10(M316) Other giant cell arteritis 95
INPAT INPAT_ICD9(7250A) Polymyalgia rheumatica 95
OUTPAT OUTPAT_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss] 94
OUTPAT OUTPAT_ICD10(M318) Other specified necrotizing vasculopathies 94
INPAT INPAT_ICD10(M349) Systemic sclerosis, unspecified 88
INPAT INPAT_ICD10(M300) Polyarteritis nodosa 87
INPAT INPAT_ICD10(M328) Other forms of systemic lupus erythematosus 87
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M32) Systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 87
INPAT INPAT_ICD10(M311) Thrombotic microangiopathy 84
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M349) Systemic sclerosis, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 80
INPAT INPAT_ICD10(M317) Microscopic polyangiitis 78
INPAT INPAT_ICD8(73491) Diffuse diseases of connective tissue, Collagenosis NUD 78
INPAT INPAT_ICD10(M339) Dermatopolymyositis, unspecified 77
OUTPAT OUTPAT_ICD10(M352) Behçet's disease 77
INPAT INPAT_ICD9(7102B) Diffuse diseases of connective tissue, Sicca syndrome 72
OUTPAT OUTPAT_ICD10(M348) Other forms of systemic sclerosis 68
INPAT INPAT_ICD9(7109X) Unspecified diffuse connective tissue disease 65
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M332) Polymyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 65
INPAT INPAT_ICD10(M320) Drug-induced systemic lupus erythematosus 61
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M316) Other giant cell arteritis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 58
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M328) Other forms of systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 58
INPAT INPAT_ICD10(M310) Hypersensitivity angiitis 56
INPAT INPAT_ICD9(7102A) Diffuse diseases of connective tissue, Sicca syndrome 55
OUTPAT OUTPAT_ICD10(M308) Other conditions related to polyarteritis nodosa 55
INPAT INPAT_ICD10(M331) Other dermatomyositis 52
INPAT INPAT_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss] 51
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M35) Other systemic involvement of connective tissue. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 50
INPAT INPAT_ICD10(M318) Other specified necrotizing vasculopathies 49
INPAT INPAT_ICD10(M355) Multifocal fibrosclerosis 49
INPAT INPAT_ICD9(4476A) Arteritis, unspecified 47
OUTPAT OUTPAT_ICD10(M32) Systemic lupus erythematosus 47
INPAT INPAT_ICD10(M308) Other conditions related to polyarteritis nodosa 45
INPAT INPAT_ICD10(M340) Progressive systemic sclerosis 45
OUTPAT OUTPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 42
OUTPAT OUTPAT_ICD10(M354) Diffuse (eosinophilic) fasciitis 41
INPAT INPAT_ICD10(M358) Other specified systemic involvement of connective tissue 37
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M339) Dermatopolymyositis, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 37
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M321) Systemic lupus erythematosus with organ or system involvement. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 35
INPAT INPAT_ICD10(M348) Other forms of systemic sclerosis 34
INPAT INPAT_ICD10(M303) Mucocutaneous lymph node syndrome [Kawasaki] 33
OUTPAT OUTPAT_ICD10(M303) Mucocutaneous lymph node syndrome [Kawasaki] 32
OUTPAT OUTPAT_ICD10(M330) Juvenile dermatomyositis 32
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M358) Other specified systemic involvement of connective tissue. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 32
INPAT INPAT_ICD10(M352) Behçet's disease 30
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M317) Microscopic polyangiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 29
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M34) Systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 29
INPAT INPAT_ICD10(M314) Aortic arch syndrome [Takayasu] 28
INPAT INPAT_ICD8(44698) Polyarteritis nodosa and allied conditions, Other 27
INPAT INPAT_ICD8(73490) Diffuse diseases of connective tissue, Keratoconjunctivitis sicca (dry eye disease). Sjögren's syndrome 27
INPAT INPAT_ICD9(7108X) Other specified diffuse diseases of connective tissue 27
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M319) Necrotizing vasculopathy, unspecified. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 27
OUTPAT OUTPAT_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere 26
OUTPAT OUTPAT_ICD10(M368) Systemic disorders of connective tissue in other diseases classified elsewhere 25
INPAT INPAT_ICD9(4462A) Hypersensitivity angiitis 24
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M301) Polyarteritis with lung involvement [Churg-Strauss]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 23
DEATH DEATH_ICD10(M313) Wegener's granulomatosis 22
DEATH DEATH_ICD10(M353) Polymyalgia rheumatica 22
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M300) Polyarteritis nodosa. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 22
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M331) Other dermatomyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 22
OUTPAT OUTPAT_ICD10(M35) Other systemic involvement of connective tissue 21
OUTPAT OUTPAT_ICD10(M362) Haemophilic arthropathy (D66-D68+) 21
INPAT INPAT_ICD8(73498) Diffuse diseases of connective tissue, Alii definiti 20
INPAT INPAT_ICD9(4465A) Giant cell arteritis 20
INPAT INPAT_ICD9(7101A) Diffuse diseases of connective tissue, Systemic sclerosis 20
INPAT INPAT_ICD10(M330) Juvenile dermatomyositis 19
INPAT INPAT_ICD10(M354) Diffuse (eosinophilic) fasciitis 19
INPAT INPAT_ICD8(71610) Polymyositis and dermatomyositis, Polymyositis 19
INPAT INPAT_ICD9(4461A) Acute febrile mucocutaneous lymph node syndrome [MCLS] 19
INPAT INPAT_ICD9(4464A) Wegener's granulomatosis 18
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M348) Other forms of systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 18
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M352) Behçet's disease. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 18
INPAT INPAT_ICD8(44638) Polyarteritis nodosa and allied conditions, Polymyalgia arteritica (rheumatica) 17
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M355) Multifocal fibrosclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 16
OUTPAT OUTPAT_ICD10(M312) Lethal midline granuloma 15
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M340) Progressive systemic sclerosis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 15
INPAT INPAT_ICD8(73499) Diffuse diseases of connective tissue, Other and unspecified 14
INPAT INPAT_ICD9(7104A) Polymyositis 14
OUTPAT OUTPAT_ICD10(M361) Arthropathy in neoplastic disease (C00-D48+) 14
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M354) Diffuse (eosinophilic) fasciitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 14
INPAT INPAT_ICD10(M362) Haemophilic arthropathy (D66-D68+) 13
INPAT INPAT_ICD8(71600) Polymyositis and dermatomyositis, Dermatomyositis 13
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M314) Aortic arch syndrome [Takayasu]. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 13
DEATH DEATH_ICD10(M332) Polymyositis 12
INPAT INPAT_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere 12
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M310) Hypersensitivity angiitis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 12
INPAT INPAT_ICD9(7103B) Diffuse diseases of connective tissue, Dermatomyositis 11
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M318) Other specified necrotizing vasculopathies. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M364) Arthropathy in hypersensitivity reactions classified elsewhere. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 11
DEATH DEATH_ICD10(M350) Sicca syndrome [Sjögren] 10
INPAT INPAT_ICD10(M368) Systemic disorders of connective tissue in other diseases classified elsewhere 10
INPAT INPAT_ICD9(4460A) Polyarteritis nodosa and allied conditions, Polyarteritis nodosa 10
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M30) Polyarteritis nodosa and related conditions. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 10
DEATH DEATH_ICD10(M329) Systemic lupus erythematosus, unspecified 9
DEATH DEATH_ICD10(M359) Systemic involvement of connective tissue, unspecified 9
INPAT INPAT_ICD10(M361) Arthropathy in neoplastic disease (C00-D48+) 9
INPAT INPAT_ICD8(44630) Polyarteritis nodosa and allied conditions, Arteritis cranialis (temporalis) 9
INPAT INPAT_ICD8(73409) Diffuse diseases of connective tissue, Sclerosis systematica NUD 9
OUTPAT OUTPAT_ICD10(M34) Systemic sclerosis 9
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M311) Thrombotic microangiopathy. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 9
INPAT INPAT_ICD8(44600) Polyarteritis nodosa and allied conditions, Polyarteritis nodosa 8
INPAT INPAT_ICD9(7103A) Diffuse diseases of connective tissue, Dermatomyositis 8
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M308) Other conditions related to polyarteritis nodosa. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 8
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M33) Dermatopolymyositis. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 8
DEATH DEATH_ICD10(M341) CR(E)ST syndrome 7
INPAT INPAT_ICD8(74310) Other congenital anomalies of nervous system, Microcephalus 7
INPAT INPAT_ICD9(4467A) Takayasu's disease 7
OUTPAT OUTPAT_ICD10(M342) Systemic sclerosis induced by drugs and chemicals 7
OUTPAT OUTPAT_ICD10(M356) Relapsing panniculitis [Weber-Christian] 7
OUTPAT OUTPAT_ICD10(M360) Dermato(poly)myositis in neoplastic disease (C00-D48+) 7
INPAT INPAT_ICD10(M356) Relapsing panniculitis [Weber-Christian] 6
INPAT INPAT_ICD8(73401) Diffuse diseases of connective tissue, Sclerosis systematica acrosclerotica 6
DEATH DEATH_ICD10(M300) Polyarteritis nodosa 5
DEATH DEATH_ICD10(M317) Microscopic polyangiitis 5
DEATH DEATH_ICD10(M331) Other dermatomyositis 5
INPAT INPAT_ICD10(M312) Lethal midline granuloma 5
INPAT INPAT_ICD9(4466A) Thrombotic microangiopathy 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M320) Drug-induced systemic lupus erythematosus. Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5
PRIM_OUT PRIM_OUT_NOT_USED_ICD10(M362) Haemophilic arthropathy (D66-D68+). Not used in endpoint definition. POSSIBLY INACCURATE IN COMPLEX ENDPOINTS! 5